Protein Name & Synonyms:
ELISA (dilution: 0.01, 0.03ug/ml), Western Blotting
This product detects a band of approximately 45kDa in human kidney cell lysates
This product specifically recognizes human ASS1 (Argininosuccinate synthetase 1), an ornithine (urea) cycle enzyme and member of the argininosuccinate synthase family, which catalyzes the penultimate step of the arginine biosynthetic pathway.
Defects in ASS1 genes are responsible for the autosomal recessive disease known as citrullinemia type 1 (CTLN1), characterized by increased levels of urine and serum citrulline, and ammonia intoxication.
This product is reported as suitable for use in immunoprecipitation studies.
Store at +4 °C or at -20 °C if preferred.
Storage in frost-free freezers is not recommended.
This product should be stored undiluted. Avoid repeated freezing and thawing as this may denature the antibody. Should this product contain a precipitate we recommend microcentrifugation before use.
If stored in this manner, this product is stable for 18 months after receipt.
Purified IgG - liquid
TRIS buffered saline
Antiserum to ASS1 was raised by repeated immunisation of goats with highly purified antigen. Purified IgG was prepared by affinity chromatography.
Peptide sequence C-ENPKNQAPPGLYTKTQD from the internal region of ASS1 (NP_000041.2; NP_446464.1).
0.02% Sodium Azide (NaN3)
0.5% Bovine Serum Albumin