Rabbit Anti-GNS (Center N189) Antibody, 400 µl
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Product Description
Specifications
| Size | 400 µL |
| Estimated Lead Time | 1-2 weeks |
| Species | Human |
| Host Species | Rabbit |
| Accession Number | P15586|Q8BFR4|Q1LZH9 |
| Gene Id | 2799 |
| Gene Symbols | GNS |
| Protein Name / Synonyms | N-acetylglucosamine-6-sulfatase, Glucosamine-6-sulfatase, G6S, GNS |
| Clonality | Polyclonal |
| Clone | RB19340 |
| Isotype | Kappa, Rabbit |
| Recommended Applications | Western Blotting, IHC-P |
| Shipping Type | Blue ice |
| Storage | -20°C |
Introduction
GNS is a lysosomal enzyme found in all cells. It is involved in the catabolism of heparin, heparan sulphate, and keratan sulphate. Deficiency of this enzyme results in the accumulation of undegraded substrate and the lysosomal storage disorder mucopolysaccharidosis type IIID (Sanfilippo D syndrome). Mucopolysaccharidosis type IIID is the least common of the four subtypes of Sanfilippo syndrome.
Other Information
NCBI Accession #
NP_002067.1
Antigen Type
Synthetic Peptide
Format
Purified polyclonal antibody supplied in PBS with 0.09% (W/V) sodium azide. This antibody is prepared by Saturated Ammonium Sulfate (SAS) precipitation followed by dialysis against PBS.
Calculated Molecular Weight (Da)
62082
Antigen Source
Human
Images
WB (1:1000)
Western blot analysis of GNS antibody (Center N189) (Cat. #102-27045) in 293 cell line lysates (35ug/lane). GNS (arrow) was detected using the purified Pab.
Storage/Stability
2-8°C (short-term); -20°C (long-term)
Expiration:
12 months from the date of shipment when stored properly.